Ewing sarcoma accounts for 3% of all pediatric malignancies1 with rib involvement accounting for 12%.2 Extension into the thoracic cavity can cause cardiopulmonary compromise. We report an eight-year-old male with dyspnea and abnormal chest findings. Chest CT scan showed a large well-defined mass occupying the right hemithorax. A right pneumonectomy was simultaneously done with excision of the mass. In a dyspneic child with an opacified hemithorax, a foremost consideration would be a mass. Early diagnosis may allow for neoadjuvant therapy, hence preventing significant morbidity associated with pneumonectomy.